* Cardiomyopathy 定義 :
先排除因為 HTN, CAD, VHD or congenital heart disease
等原因所造成的次發性心肌病變
DCM : 壁薄, 四腔室擴大 , Systolic dysfunction
HCM : 不對稱中膈肥厚 (中膈/後壁>1.3)
LV 變超小 , Diastolic dysfunction
Gene(AD), mitral valve SAM => LVOT obstruction
beta blocker, CCB
RCM : 壁變硬, Diastolic dysfunction, Infiltrative, Treat reason
*** SAM 示意圖 ***
HOCM 特色 :
1. Systolic anterior motion (SAM) of the mitral valve
and dynamic left ventricular outflow tract (LVOT) obstruction
2. Asymmetrical thickening of the anterior interventricular septum
(Asymmetrical septal hypertrophy)
- DCM : CHF symptoms
- HCM : Syncope, Sudden death
- RCM : DOE, Fatigue
* HCM EKG :
- Deep, narrow (dagger-like)“Septal Q waves” in the lateral and sometimes inferior leads
(Due to the abnormally hypertrophied interventricular septum)
下壁 + 外側壁 --- > Q wave
- LVH
- 大 R 波 lead T inv
- Sometimes associated with WPW
- P mitrale (LAE) : Left ventricular diastolic dysfunction
HCM :
- Exertional syncope or pre-syncope
suggesting dynamic LVOT obstruction ± ventricular dysrhythmia,
with the potential for sudden cardiac death.
- Symptoms of pulmonary congestion due to left ventricular dysfunction
(exertional dyspnoea, fatigue, orthopnoea, paroxysmal nocturnal dyspnoea)
- Chest pain may be typical anginal pain due to increased demand (thicker myocardial walls)
and reduced supply (aberrant coronary arteries).
- Palpitations due to supraventricular or ventricular arrhythmias.
* HCM :
* DCM :
* HCM Mamagement :
- Restriction of physical activity ( 只能輕度中度有氧運動 )
- Implantable cardioverter-defibrillators ( ICD )
- Nonpharmacologictreatment of LVOT obstruction
- Medical treatment : Beta-blocker, CCB
- Catheter ablation
* 水多水少?
回心血流增加 : 蹲姿, 肌肉收縮, 吸氣 (胸內負壓增加->靜脈回流增加)
回心血流減少 : 站姿, valsava maneuver, 吐氣
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